One in every hundred babies born has a heart condition. This makes Congenital Heart Disease the most common birth defect in Australia. There are approximately 40 identifiable birth anomalies and syndromes that are classified as Congenital Heart Disease.
The table below lists Congenital Heart Disease as described in the WHO International Classification of Diseases code. The list is sorted from most common (VSD) to the rarest conditions. For more information on individual disorders, including statistics based on the National Perinatal Statistics Unit (Australia) data for 1981-97, select an entry from the table.
| · Eisenmenger's defect or complex
· Gerbode defect · Interventricular septal defect · Left ventricular-right atrial communication · Roger's disease
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| Total Births 1981-97: 6703 | Rate per 10 000 births: 16.2 |
| · Patent ductus Botalli
· Persistent ductus arteriosus
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| Total Births 1981-97: | Rate per 10 000 births: |
| · Defect: atrium Secundum fossa ovalis· Lutembacher's syndrome
· Patent or persistent: foramen ovale ostium secundum
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| Total Births 1981-97: 2068 | Rate per 10 000 births: 5.0 |
| [745.10]: Complete Transposition of Great Vessels (TGV)
· NOS · Classical [745.11]: Double outlet right ventricle (DORV) · Dextratransposition of aorta · Incomplete transposition of great vessels · Origin of both great vessels from right ventricle · Taussig-Bing syndrome or defect [745.12]: Corrected transposition of great vessels (CCTGA) [745.19]: Other
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| Total Births 1981-97: 1474 | Rate per 10 000 births: 3.6 |
| [747.10]: Coarctation of aorta (preductal) (postductal)
· Hypoplasia of aortic arch [747.11]: Interruption of aortic arch
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| Total Births 1981-97: 1474 | Rate per 10 000 births: 3.6 |
| Atresia, or marked hypoplasia, of aortic orifice or valve, with hypoplasia of ascending aorta and defective development of left ventricle (with mitral valve atresia).
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| Total Births 1981-97: 923 | Rate per 10 000 births: 2.2 |
| [746.01]: Atresia
· Congenital absence of pulmonary valve
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| Total Births 1981-97: 916 | Rate per 10 000 births: 2.2 |
| [745.60]: Endocardial cushion defect, unspecified type
[745.61]: Ostium primum defect · ersistent ostium primum [745.69]: Other · Absence of atrial septum · Atrioventricular canal type ventricular septal defect · Common atrioventricular canal · Common atrium
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| Total Births 1981-97: 825 | Rate per 10 000 births: 2.0 |
| [746.81]: Subaortic stenosis
[746.82]: Cor triatriatum [746.83]: Infundibular pulmonic stenosis · Subvalvular pulmonic stenosis [746.84]: Obstructive anomalies of heart, NEC · Uhl's disease [746.85]: Coronary artery anomaly · Anomalous origin or communication of coronary artery · Arteriovenous malformation of coronary artery · Coronary artery: o Absence o Arising from aorta or pulmonary trunk o Single [746.86]: Congenital heart block · Complete or incomplete atrioventricular [AV] block [746.87]]: Malposition of heart and cardiac apex · Abdominal heart · Dextrocardia · Ectopia cordis · Levocardia (isolated) · Mesocardia [746.8:] Other · Atresia of cardiac vein · Hypoplasia of cardiac vein · Congenital: o Cardiomegaly o Diverticulum, left ventricle o Pericardial defect
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| Total Births 1981-97: 728 | Rate per 10 000 births: 1.8 |
| [745.2]: Tetralogy of Fallot
· Fallot's pentalogy · Ventricular septal defect with pulmonary stenosis or atresia, dextraposition of aorta, and hypertrophy of right ventricle
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| Total Births 1981-97: 724 | Rate per 10 000 births: 1.7 |
| Absence of tricuspid valve
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| Total Births 1981-97: 567 | Rate per 10 000 births: 1.4 |
| [746.3]: Congenital Aortic Stenosis
[746.4]: Congenital insufficiency of aortic valve · Bicuspid aortic valve · Congenital aortic insufficiency
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| Total Births 1981-97: 557 | Rate per 10 000 births: 1.3 |
| [746.00]: Pulmonary valve anomaly, unspecified
[746.01]: Atresia, congenital · Congenital absence of pulmonary valve [746.02]: Stenosis, congenital [746.09]: Other · Congenital insufficiency of pulmonary valve · Fallot's triad or trilogy
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| Total Births 1981-97: 519 | Rate per 10 000 births: 1.3 |
| [747.20]: Anomaly of aorta, unspecified
[747.21]: Anomalies of aortic arch · Anomalous origin, right subclavian artery · Dextraposition of aorta · Double aortic arch · Kommerell's diverticulum · Overriding aorta · Persistant: convolutions, aortic arch, c right aortic arch · Vascular ring [747.22]: Atresia and stenosis of aorta · Absence of aorta · Aplasia of aorta · Hypoplasia of aorta · Stricture of aorta · Supra (valvular)-aortic stenosis [747.29]: Other · Aneurysm of sinus of Valsalva · Congenital: o Aneurysm of aorta o Dilation of aorta
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| Total Births 1981-97: 491 | Rate per 10 000 births: 1.2 |
| · Agenesis of pulmonary artery
· Anomaly of pulmonary artery · Atresia of pulmonary artery · Coarctation of pulmonary artery · Hypoplasia of pulmonary artery · Stenosis of pulmonary artery · Pulmonary arteriovenous aneurysm
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| Total Births 1981-97: 436 | Rate per 10 000 births: 1.1 |
| [747.40]: Anomaly of great veins, unspecified
· Anomaly NOS of: o Pulmonary veins o Vena cava [747.41]: Total anomalous pulmonary venous connection · Total anomalous pulmonary venous return (APVR): o Subdiaphragmatic o Supradiaphragmatic [747.42]: Partial anomalous pulmonary venous connection · Partial anomalous pulmonary venous return [747.49]: Other anomalies of great veins · Absence of vena cava (inferior) (superior) · Stenosis of vena cava (inferior) (superior) · Persistent: o Left posterior cardinal vein o Left superior vena cava · Scimitar syndrome · Transposition of pulmonary veins NOS
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| Total Births 1981-97: 435 | Rate per 10 000 births: 1.1 |
| {746.5]: Congenital mitral stenosis
· Fused commissure of mitral valve · Parachute deformity of mitral valve · Supernumerary cusps of mitral valve [746.6]: Congenital mitral insufficiency
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| Total Births 1981-97: 338 | Rate per 10 000 births: 0.8 |
| Congenital:
· Anomaly of heart NOS · Heart disease NOS
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| Total Births 1981-97: 321 | Rate per 10 000 births: 0.8 |
| · Absent septum between aorta and pulmonary artery
· Communication (abnormal) between aorta and pulmonary artery · Aortic septal defect · Common aortopulmonary trunk · Persistent truncus arteriosus
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| Total Births 1981-97: 271 | Rate per 10 000 births: 0.7 |
| · Cor triloculare biatriatum
· Single ventricle |
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| Total Births 1981-97: 251 | Rate per 10 000 births: 0.6 |
| Ebstein's anomaly
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| Total Births 1981-97: 137 | Rate per 10 000 births: 0.3 |
| [745.7]: Cor Biloculare
· Absence of atrial and ventricular septa [745.8]: Other [745.9]: Unspecified defect of septal closure · Unspecified defect of Septal Closure · Septal defect NOS
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| Total Births 1981-97: 62 | Rate per 10 000 births: .01 |